Pseudomyxoma peritonei is a rare disease presenting massive mucinous ascites and it is usually associated with mucocele of the appendix, ovarian cystadenoma and cystadenocarcinoma. The term "pseudomyxoma peritonei" was originated by Werth in
1884.
Pseudomyxoma peritonei is usually presented in the peritoneal cavity, lymphatics, and parenchymal tissue. He disease is rarely spread extraperitoneally.
We experienced two cases of pseudomyxoma peritonei. They are 51-year-old male and 70-year-old female presented with marked abdominal distension, indigestion and abdominal discomfort. Abdominal ultrasonogram showed inhomogenous material occupied
in
the
whole abdominal cavity with displacement of the solid organ. Abdominal CT scan showed septated low attenuation material in central. We suggested pseudomyxoma peritonei clinically and were confirmed by surgery. At laparotomy the abdomen, was
filled
with
thick gelatinous mucoid material having internal septation, the bowel was encased in mucin. Loculated mucinous cyst are present in the appedix, ovaries and mucin globules are found within the omentum. In first case, appendectomy and aggressive
debulking
of intraperitoneal tumor was done and second case was treated with bilateral salphingo-oophorectomy, tumor resection and postoperative chemotherapy using 5-FU and mitomycin. Up to the present, they no evidence of recurrence. (Korea J
Gastreoenterol
1994
; 26 : 393-398)
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